: Systemic autoinflammatory diseases (SAIDs) are disorders of innate immunity, which are characterized by unprovoked recurrent flares of systemic inflammation often characterized by fever associated with clinical manifestations mainly involving the musculoskeletal, mucocutaneous, gastrointestinal, and nervous systems. Several conditions also present with varied, sometimes prominent, involvement of the vascular system, with features of vasculitis characterized by variable target vessel involvement and organ damage. Here, we report a systematic review of vasculitis and vasculopathy associated with inborn errors of immunity.
Vasculitis and vasculopathy associated with inborn errors of immunity: an overview / Federici, Silvia; Cinicola, Bianca Laura; La Torre, Francesco; Castagnoli, Riccardo; Lougaris, Vassilios; Giardino, Giuliana; Volpi, Stefano; Caorsi, Roberta; Leonardi, Lucia; Corrente, Stefania; Soresina, Annarosa; Cancrini, Caterina; Insalaco, Antonella; Gattorno, Marco; De Benedetti, Fabrizio; Marseglia, Gian Luigi; Del Giudice, Michele Miraglia; Cardinale, Fabio. - In: FRONTIERS IN PEDIATRICS. - ISSN 2296-2360. - 11:(2023). [10.3389/fped.2023.1258301]
Vasculitis and vasculopathy associated with inborn errors of immunity: an overview
Cinicola, Bianca LauraCo-primo
;Leonardi, Lucia;Del Giudice, Michele Miraglia;
2023
Abstract
: Systemic autoinflammatory diseases (SAIDs) are disorders of innate immunity, which are characterized by unprovoked recurrent flares of systemic inflammation often characterized by fever associated with clinical manifestations mainly involving the musculoskeletal, mucocutaneous, gastrointestinal, and nervous systems. Several conditions also present with varied, sometimes prominent, involvement of the vascular system, with features of vasculitis characterized by variable target vessel involvement and organ damage. Here, we report a systematic review of vasculitis and vasculopathy associated with inborn errors of immunity.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
