A 79-year-old woman underwent surgical resection of a peripheral, solitary, pulmonary lesion that was diagnosed as malignant PEComa. Her clinical history was positive for uterine leiomyosarcoma, excised 20 years before. Re-evaluation of the primary uterine lesion led to the final diagnosis of lung metastasis from uterine PEComa. While long latency between primary tumour and metastasis is a known and characteristic feature of PEComas, a 20-year interval is unprecedented in the literature.

Extremely late-onset pulmonary metastasis from uterine PEComa / Ascione, Andrea; Martignoni, Guido; D'Amati, Giulia; Della Rocca, Carlo; Graziano, Paolo; Pernazza, Angelina. - In: PATHOLOGICA. - ISSN 1591-951X. - 114:4(2022), pp. 312-315. [10.32074/1591-951X-762]

Extremely late-onset pulmonary metastasis from uterine PEComa

Ascione, Andrea
Primo
;
d'Amati, Giulia;Della Rocca, Carlo;Graziano, Paolo
Penultimo
;
Pernazza, Angelina
Ultimo
2022

Abstract

A 79-year-old woman underwent surgical resection of a peripheral, solitary, pulmonary lesion that was diagnosed as malignant PEComa. Her clinical history was positive for uterine leiomyosarcoma, excised 20 years before. Re-evaluation of the primary uterine lesion led to the final diagnosis of lung metastasis from uterine PEComa. While long latency between primary tumour and metastasis is a known and characteristic feature of PEComas, a 20-year interval is unprecedented in the literature.
2022
PEComa; lung; metastases; soft tissues; uterus; aged; female; humans; lung neoplasms; perivascular epithelioid cell neoplasms; uterine neoplasms
01 Pubblicazione su rivista::01i Case report
Extremely late-onset pulmonary metastasis from uterine PEComa / Ascione, Andrea; Martignoni, Guido; D'Amati, Giulia; Della Rocca, Carlo; Graziano, Paolo; Pernazza, Angelina. - In: PATHOLOGICA. - ISSN 1591-951X. - 114:4(2022), pp. 312-315. [10.32074/1591-951X-762]
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11573/1657748
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