Introduction: Behçet disease (BD) is a chronic relapsing inflammatory disease of unknown etiology, characterized by variable clinical manifestations. Methods: A 28-year-old woman with BD Cardiovascular and Bipolar Disorder underwent emergency surgical treatment of ascending aortic pseudoaneurysm for ruptured right coronary ostium.A modified Bentall procedure with tricuspid annuloplasty, surgical thrombectomy, and a single coronary artery bypass using a saphenous vein graft was performed. A biological prosthesis was used initially but subsequently deteriorated. We then successfully performed a valve-in-valve (ViV) transcatheter aortic valve implantation (TAVI). Results: The postoperative recovery was uneventful and at follow-up, two years post valve procedure, the patient was completely symptom-free. She remains under long-term medical surveillance. Conclusion: The management of BD with cardiac involvement must be led by a multidisciplinary team.
Postinflammatory rupture of right coronary artery ostium complicating Behçet disease / Fiore, A.; Piscitelli, M.; Rabia, A.; Derbel, H.; Bergoend, E.; Avtaar Singh, S. S.; Nappi, F.. - In: JOURNAL OF CARDIAC SURGERY. - ISSN 0886-0440. - 37:10(2022), pp. 3432-3435. [10.1111/jocs.16771]
Postinflammatory rupture of right coronary artery ostium complicating Behçet disease
Fiore A.
Primo
Conceptualization
;
2022
Abstract
Introduction: Behçet disease (BD) is a chronic relapsing inflammatory disease of unknown etiology, characterized by variable clinical manifestations. Methods: A 28-year-old woman with BD Cardiovascular and Bipolar Disorder underwent emergency surgical treatment of ascending aortic pseudoaneurysm for ruptured right coronary ostium.A modified Bentall procedure with tricuspid annuloplasty, surgical thrombectomy, and a single coronary artery bypass using a saphenous vein graft was performed. A biological prosthesis was used initially but subsequently deteriorated. We then successfully performed a valve-in-valve (ViV) transcatheter aortic valve implantation (TAVI). Results: The postoperative recovery was uneventful and at follow-up, two years post valve procedure, the patient was completely symptom-free. She remains under long-term medical surveillance. Conclusion: The management of BD with cardiac involvement must be led by a multidisciplinary team.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
