We describe the case of a boy with spondyloepiphyseal dysplasia congenita. At birth, he experienced severe respiratory distress necessitating tracheotomy. Endoscopy done because mechanical ventilation failed to resolve desaturations disclosed severe tracheo-bronchomalacia. A Polyflex silicone stent was placed in the trachea (replaced by Y-Dumon stent) and 2 Palmaz metallic stents in the mainstem bronchi (overlapped with 2 Jomed stents 5 years later). Airway stenting guaranteed a suitable respiratory status and allowed a child who was expected to die at birth, to reach 13.5 years old in good conditions.

Airway stenting in a child with spondyloepiphyseal dysplasia congenita: 13-year survival / Nenna, Raffaella; Midulla, Fabio; Masi, Laura; Bacci, Giacomo Maria; Frassanito, Antonella; Baggi, Roberto; Brandi, Maria Luisa; Avenali, Stefano; Mirabile, Lorenzo; Serio, Paola. - In: INTERNATIONAL JOURNAL OF PEDIATRIC OTORHINOLARYNGOLOGY. - ISSN 0165-5876. - 99:(2017), pp. 13-16. [10.1016/j.ijporl.2017.05.008]

Airway stenting in a child with spondyloepiphyseal dysplasia congenita: 13-year survival

Nenna, Raffaella
;
Midulla, Fabio;MASI, LAURA;Frassanito, Antonella;
2017

Abstract

We describe the case of a boy with spondyloepiphyseal dysplasia congenita. At birth, he experienced severe respiratory distress necessitating tracheotomy. Endoscopy done because mechanical ventilation failed to resolve desaturations disclosed severe tracheo-bronchomalacia. A Polyflex silicone stent was placed in the trachea (replaced by Y-Dumon stent) and 2 Palmaz metallic stents in the mainstem bronchi (overlapped with 2 Jomed stents 5 years later). Airway stenting guaranteed a suitable respiratory status and allowed a child who was expected to die at birth, to reach 13.5 years old in good conditions.
2017
airway; bronchial stents; pediatric; spondyloepiphyseal dysplasia congenita
01 Pubblicazione su rivista::01i Case report
Airway stenting in a child with spondyloepiphyseal dysplasia congenita: 13-year survival / Nenna, Raffaella; Midulla, Fabio; Masi, Laura; Bacci, Giacomo Maria; Frassanito, Antonella; Baggi, Roberto; Brandi, Maria Luisa; Avenali, Stefano; Mirabile, Lorenzo; Serio, Paola. - In: INTERNATIONAL JOURNAL OF PEDIATRIC OTORHINOLARYNGOLOGY. - ISSN 0165-5876. - 99:(2017), pp. 13-16. [10.1016/j.ijporl.2017.05.008]
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11573/1187819
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