Klippel-Feil syndrome is a rare disease with congenital musculoskeletal condition characterized by faulty segmentation of cervical vertebrae and consists of cervical vertebra fusions with limitation of head movements, short neck and low posterior hairline. In several cases the syndrome is associated with cardiovascular malformations. Patients affected by Klippel-Feil syndrome could be an anesthetic challenge, not only during cardiac surgery. We are presenting a case of Klippel-Feil Syndrome in an adult patient, who was operated on for a pulmonary valve insufficiency in a previously corrected Tetralogy of Fallot Syndrome. We are going to discuss the features of this rare syndrome.

Klippel-Feil syndrome. When using fiberoptic bronchoscopy guide, a case report / Bizzarri, Federico; Dralov, Andriy; Segreto, Antonio; Maria Sole, Cantarano; De Siena, Paolo; Pinto Luca, Di; Congiu, Stefano; Van Doorn, Caren; Carini, Luisa. - In: CLINICS IN SURGERY. - ISSN 2474-1647. - ELETTRONICO. - 2:(2017), pp. 1-3.

Klippel-Feil syndrome. When using fiberoptic bronchoscopy guide, a case report

Federico Bizzarri
Writing – Original Draft Preparation
;
Luisa Carini
Supervision
2017

Abstract

Klippel-Feil syndrome is a rare disease with congenital musculoskeletal condition characterized by faulty segmentation of cervical vertebrae and consists of cervical vertebra fusions with limitation of head movements, short neck and low posterior hairline. In several cases the syndrome is associated with cardiovascular malformations. Patients affected by Klippel-Feil syndrome could be an anesthetic challenge, not only during cardiac surgery. We are presenting a case of Klippel-Feil Syndrome in an adult patient, who was operated on for a pulmonary valve insufficiency in a previously corrected Tetralogy of Fallot Syndrome. We are going to discuss the features of this rare syndrome.
2017
Klippel-Feil syndrome; anesthesia; cardiac surgery; tetralogy of fallot; intubation; vertebral fusion
01 Pubblicazione su rivista::01i Case report
Klippel-Feil syndrome. When using fiberoptic bronchoscopy guide, a case report / Bizzarri, Federico; Dralov, Andriy; Segreto, Antonio; Maria Sole, Cantarano; De Siena, Paolo; Pinto Luca, Di; Congiu, Stefano; Van Doorn, Caren; Carini, Luisa. - In: CLINICS IN SURGERY. - ISSN 2474-1647. - ELETTRONICO. - 2:(2017), pp. 1-3.
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11573/1113761
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