Osteogenesi imperfetta in età pediatrica

Objective: The aim of study want early know on hearing loss in the children with osteogenesis imperfecta. Materials and method: The study deals with 15 cases of progressive deafness in patients with abnormalities in growth and skeletal disease, suffering from osteogenesis imperfecta. The study is clinical and audiological research and for the progressive nature of the patology the AA. recommend the necessity of a screening service to detect early hearing loss in the paediatric population with osteogenesis imperfecta. Results: Fifteen children (30 ears) were observed: 14 ears have normal hearing; 9 ears have conductive hearing loss; 7 have sensorineural hearing loss. Conclusions: The treatment is the hearing aid and where possible the surgery of the stapes with caution. this study ould suggest that routine screening is worthwhile in children with osteogenesis imperfecta.