Bilateral striopallidodentate calcification, usually termed Fahr's disease, can give rise to various clinical manifestations including hyperkinetic movement disorders or a hypokinetic Parkinsonian syndrome, behavioural and mood changes, cognitive deficits and even frank dementia. We describe four patients all of whom underwent a detailed scintigraphic, neuroradiological and clinical work-up: two had primary, sporadic Fahr's disease and two had Fahr's disease secondary to hypoparathyroidism. The neuroradiological and clinical studies disclosed similar anatomical and pathological changes in the four patients but variable and sometimes unexpected clinical manifestations. Both patients with primary forms had hypokinetic Parkinsonian syndrome, both patients with secondary forms had hyperkinetic movements. Dopamine autotransporter scan brain scintigraphy disclosed an unexpected unilateral putamen involvement despite substantially symmetric calcifications. © 2010 Springer-Verlag.

Scintigraphic, neuroradiological and clinical comparison in two patients with primary sporadic and two with secondary Fahr's disease / Giovanni, Caranci; Giovanni, Grillea; Francesco, Barbato; Alexandra, Brunetti; Tiziana, Tassinari; Mariarita Di Ruzza, ; Lena, Francesco; Barbara, Gandolfi; Anna Elisa Castellano, ; Marcello, Bartolo; Colonnese, Claudio; Nicola, Modugno; Stefano, Ruggieri; Mario, Manfredi. - In: NEUROLOGICAL SCIENCES. - ISSN 1590-1874. - 32:2(2011), pp. 337-341. [10.1007/s10072-010-0444-9]

Scintigraphic, neuroradiological and clinical comparison in two patients with primary sporadic and two with secondary Fahr's disease

Francesco Lena;COLONNESE, Claudio;
2011

Abstract

Bilateral striopallidodentate calcification, usually termed Fahr's disease, can give rise to various clinical manifestations including hyperkinetic movement disorders or a hypokinetic Parkinsonian syndrome, behavioural and mood changes, cognitive deficits and even frank dementia. We describe four patients all of whom underwent a detailed scintigraphic, neuroradiological and clinical work-up: two had primary, sporadic Fahr's disease and two had Fahr's disease secondary to hypoparathyroidism. The neuroradiological and clinical studies disclosed similar anatomical and pathological changes in the four patients but variable and sometimes unexpected clinical manifestations. Both patients with primary forms had hypokinetic Parkinsonian syndrome, both patients with secondary forms had hyperkinetic movements. Dopamine autotransporter scan brain scintigraphy disclosed an unexpected unilateral putamen involvement despite substantially symmetric calcifications. © 2010 Springer-Verlag.
2011
hypoparathyroidism; fahr's disease; hyperkinetic movements; functional imaging
01 Pubblicazione su rivista::01a Articolo in rivista
Scintigraphic, neuroradiological and clinical comparison in two patients with primary sporadic and two with secondary Fahr's disease / Giovanni, Caranci; Giovanni, Grillea; Francesco, Barbato; Alexandra, Brunetti; Tiziana, Tassinari; Mariarita Di Ruzza, ; Lena, Francesco; Barbara, Gandolfi; Anna Elisa Castellano, ; Marcello, Bartolo; Colonnese, Claudio; Nicola, Modugno; Stefano, Ruggieri; Mario, Manfredi. - In: NEUROLOGICAL SCIENCES. - ISSN 1590-1874. - 32:2(2011), pp. 337-341. [10.1007/s10072-010-0444-9]
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11573/74635
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