Pierre Robin Sequence (PRS) is a congenital abnormality characterized by mandibular hypoplasia, glossoptosis and often secondary palate cleft. It may be an isolated or part of a most complicated syndrome. The genetic syndrome that most frequently co-occurs is Stickler syndrome characterized by skeletal abnormalities, joint pain, congenital myopia and retinal detachment. The authors describe their fast and early mandibular osteodistraction (FEMOD) protocol in severe cases of PRS airway obstruction. © 2014 European Association for Cranio-Maxillo-Facial Surgery.
Fast and early mandibular osteodistraction (FEMOD) in severe Pierre Robin Sequence / Cascone, Piero; Papoff, Paola; Arangio, Paolo; Vellone, Valentino; Calafati, Vincenzo; Silvestri, Alessandro. - In: JOURNAL OF CRANIO-MAXILLOFACIAL SURGERY. - ISSN 1010-5182. - 42:(2014), pp. 1364-1370. [10.1016/j.jcms.2014.03.027]
Fast and early mandibular osteodistraction (FEMOD) in severe Pierre Robin Sequence
CASCONE, PIERO;PAPOFF, PAOLA;ARANGIO, PAOLO;VELLONE, VALENTINO;CALAFATI, VINCENZO;SILVESTRI, ALESSANDRO
2014
Abstract
Pierre Robin Sequence (PRS) is a congenital abnormality characterized by mandibular hypoplasia, glossoptosis and often secondary palate cleft. It may be an isolated or part of a most complicated syndrome. The genetic syndrome that most frequently co-occurs is Stickler syndrome characterized by skeletal abnormalities, joint pain, congenital myopia and retinal detachment. The authors describe their fast and early mandibular osteodistraction (FEMOD) protocol in severe cases of PRS airway obstruction. © 2014 European Association for Cranio-Maxillo-Facial Surgery.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
