Coat's like disease associated to retinitis pigmentosa: Casual association or inherited defect?

Coat’s like disease was observed in literature in different incidence up 3,6% of patients. Our experience shows that even if microteleangectasies are frequently observed in tapetoretinal degenerations exudation and retinal detachment are less frequent, only to these two main symtoms are specifically present in the Coat’s like disease. Moreover these findings are not inherited in fact in our pedigree only two patients on ten had this charachteristic, so we think that, as observed in other cases of chorio-retinal scars, a vascular shunt between choriocapillary and retinal system may cause a surcharge of blood flow in the capillary network starting the exudative response. In this view we consider that Coat’s like disease and Retinitis Pigmentosa are two different entities casually associated.