Oncogenic osteomalacia is an uncommon syndrome characterized by bone pain, proximal muscle weakness, hypophosphatemia, hyperphosphaturia, and a low plasma concentration of 1,25-dihydroxy-vitamin D. The disease affects both sexes at around 40 years of age, although it can sometimes affect children and adolescents. Generally, the syndrome is associated with a tumor, usually benign, of mesenchymal origin and is resolved after removal of the tumor; this syndrome can sometimes be associated with malignant tumors. These tumors seem to be histologically heterogeneous and are generally localized in soft tissues and bone. In this article, a case of oncogenic osteomalacia associated with a hypophosphaturic mesenchymal tumor of the ethmoid is reported in a 24-year-old man. After surgical and radical removal of the tumor, the patient noted a decrease in the clinical symptoms and signs.

Hypophosphaturic mesenchymal tumor of the ethmoid associated with oncogenic osteomalacia / Ungari, Claudio; Giovanni, Rocchi; Rinna, Claudio; Agrillo, Alessandro; Alessandro, Lattanzi; Pagnoni, Mario. - In: THE JOURNAL OF CRANIOFACIAL SURGERY. - ISSN 1049-2275. - STAMPA. - 15:3(2004), pp. 523-527. [10.1097/00001665-200405000-00036]

Hypophosphaturic mesenchymal tumor of the ethmoid associated with oncogenic osteomalacia

UNGARI, Claudio;Claudio Rinna;AGRILLO, Alessandro;PAGNONI, MARIO
2004

Abstract

Oncogenic osteomalacia is an uncommon syndrome characterized by bone pain, proximal muscle weakness, hypophosphatemia, hyperphosphaturia, and a low plasma concentration of 1,25-dihydroxy-vitamin D. The disease affects both sexes at around 40 years of age, although it can sometimes affect children and adolescents. Generally, the syndrome is associated with a tumor, usually benign, of mesenchymal origin and is resolved after removal of the tumor; this syndrome can sometimes be associated with malignant tumors. These tumors seem to be histologically heterogeneous and are generally localized in soft tissues and bone. In this article, a case of oncogenic osteomalacia associated with a hypophosphaturic mesenchymal tumor of the ethmoid is reported in a 24-year-old man. After surgical and radical removal of the tumor, the patient noted a decrease in the clinical symptoms and signs.
2004
ethmoid tumor; hypophosphatemia; osteomalacia
01 Pubblicazione su rivista::01a Articolo in rivista
Hypophosphaturic mesenchymal tumor of the ethmoid associated with oncogenic osteomalacia / Ungari, Claudio; Giovanni, Rocchi; Rinna, Claudio; Agrillo, Alessandro; Alessandro, Lattanzi; Pagnoni, Mario. - In: THE JOURNAL OF CRANIOFACIAL SURGERY. - ISSN 1049-2275. - STAMPA. - 15:3(2004), pp. 523-527. [10.1097/00001665-200405000-00036]
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11573/363791
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