Aims and background: Multiple endocrine neoplasia (MEN) syndromes include a group of disorders characterized by the neoplastic transformation of two or more endocrine tissues. In type 1 syndrome (MEN-1), pituitary, parathyroid and pancreatic islet tumors are most frequently represented. Thymic neoplasms are also rarely associated, and thymectomy during subtotal or total parathyroidectomy should always be considered. Study design: The authors describe a rare case of a 22-year-old male who presented a type B1 thymoma without myasthenia gravis associated to hyperparathyroidism, corticoadrenal adenoma and three neuroendocrine pancreatic lesions (somatostatinoma, glucagonoma and insulinoma).
Type B1 thymoma in multiple endocrine neoplasia type 1 (MEN-1) syndrome / DE TOMA, Giorgio; M., Plocco; Nicolanti, Virgilio; Brozzetti, Stefania; Letizia, Claudio; Cavallaro, Antonino. - In: TUMORI. - ISSN 0300-8916. - 87:(2001), pp. 266-268.
Type B1 thymoma in multiple endocrine neoplasia type 1 (MEN-1) syndrome
DE TOMA, Giorgio;NICOLANTI, Virgilio;BROZZETTI, Stefania;LETIZIA, Claudio;CAVALLARO, Antonino
2001
Abstract
Aims and background: Multiple endocrine neoplasia (MEN) syndromes include a group of disorders characterized by the neoplastic transformation of two or more endocrine tissues. In type 1 syndrome (MEN-1), pituitary, parathyroid and pancreatic islet tumors are most frequently represented. Thymic neoplasms are also rarely associated, and thymectomy during subtotal or total parathyroidectomy should always be considered. Study design: The authors describe a rare case of a 22-year-old male who presented a type B1 thymoma without myasthenia gravis associated to hyperparathyroidism, corticoadrenal adenoma and three neuroendocrine pancreatic lesions (somatostatinoma, glucagonoma and insulinoma).I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
