Perivascular epithelioid cell tumors (PEComas) in the pediatric population are very rare and frequently arise in the gastrointestinal tract. These tumors are characterized by variable morphological and immunohistochemical features, which may pose significant problems in differential diagnosis with other gastrointestinal mesenchymal tumors in pediatric patients. In presenting an unusual pediatric case of gastrointestinal PEComa, we also discuss the possible differential diagnosis of this rare entity
Pediatric gastrointestinal PEComas: a diagnostic challenge / Pizzi, Marco; di Lorenzo, I; d'Amore, Es; D'Angelo, P; Alaggio, Rita. - In: PEDIATRIC AND DEVELOPMENTAL PATHOLOGY. - ISSN 1093-5266. - 17(5):(2014), pp. 406-408. [10.2350/14-06-1501-CR.1]
Pediatric gastrointestinal PEComas: a diagnostic challenge
ALAGGIO, RITA
2014
Abstract
Perivascular epithelioid cell tumors (PEComas) in the pediatric population are very rare and frequently arise in the gastrointestinal tract. These tumors are characterized by variable morphological and immunohistochemical features, which may pose significant problems in differential diagnosis with other gastrointestinal mesenchymal tumors in pediatric patients. In presenting an unusual pediatric case of gastrointestinal PEComa, we also discuss the possible differential diagnosis of this rare entityI documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
