Pancreatic cystosis (PC) is an uncommon manifestation of pancreas involvement in cystic fibrosis (CF), characterized by the presence of multiple macrocysts partially or completely replacing pancreas. Only few reports are available from literature and management (surgery vs follow up) is commonly based on the presence of symptoms or complications due to local mass effect, although evidence-based recommendations are still not available. We here report the case of a young adult CF patient with PC, in which cardiopulmonary exercise testing (CPET) provided important information to be integrated to the radiological finding of inferior vena cava compression by the multicystic pancreas complex. Through the analysis of oxygen kinetic cardiodynamic phase pattern, CPET may be helpful to safely exclude significant mass effects on blood venous return and to improve the decision-making process on whether to consider surgery or not in patients with PC.

Pancreatic cystosis in cystic fibrosis. Sometimes a bike ride can help you decide / Di Paolo, M.; Di Gaeta, A.; Indino, E. L.; Mordenti, M.; Palange, P.. - In: RESPIRATORY MEDICINE CASE REPORTS. - ISSN 2213-0071. - 29:(2020), pp. 1-5. [10.1016/j.rmcr.2020.101018]

Pancreatic cystosis in cystic fibrosis. Sometimes a bike ride can help you decide

Di Paolo M.
Primo
;
Di Gaeta A.;Indino E. L.;Mordenti M.;Palange P.
Ultimo
2020

Abstract

Pancreatic cystosis (PC) is an uncommon manifestation of pancreas involvement in cystic fibrosis (CF), characterized by the presence of multiple macrocysts partially or completely replacing pancreas. Only few reports are available from literature and management (surgery vs follow up) is commonly based on the presence of symptoms or complications due to local mass effect, although evidence-based recommendations are still not available. We here report the case of a young adult CF patient with PC, in which cardiopulmonary exercise testing (CPET) provided important information to be integrated to the radiological finding of inferior vena cava compression by the multicystic pancreas complex. Through the analysis of oxygen kinetic cardiodynamic phase pattern, CPET may be helpful to safely exclude significant mass effects on blood venous return and to improve the decision-making process on whether to consider surgery or not in patients with PC.
2020
cardiodynamic component; cardiopulmonary exercise testing; cystic fibrosis; oxygen kinetics; pancreatic cystosis
01 Pubblicazione su rivista::01a Articolo in rivista
Pancreatic cystosis in cystic fibrosis. Sometimes a bike ride can help you decide / Di Paolo, M.; Di Gaeta, A.; Indino, E. L.; Mordenti, M.; Palange, P.. - In: RESPIRATORY MEDICINE CASE REPORTS. - ISSN 2213-0071. - 29:(2020), pp. 1-5. [10.1016/j.rmcr.2020.101018]
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11573/1399384
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