Erickson, Robert Porter
Erickson, Robert Porter
DIPARTIMENTO DI PSICOLOGIA
A novel approach to treat mitochondrial metabolism dysfunction in Niemann-Pick type C disease
2024 Tiberi, Jessica; Stefanelli, Roberta; Trenta, Francesco; LA ROSA, Piergiorgio; Siddlesh, Aras; Erickson, Robert; Grossmann, Lawrence I.; Fiorenza, Maria Teresa
Altered Shh signaling at the primary cilium is responsible for abnormal cerebellum morphogenesis in Niemann-Pick C1 (NPC1) disease.
2016 Canterini, Sonia; Caporali, Paola; Bruno, Francesco; Dragotto, Jessica; Palladino, Giampiero; Dardis, A; Erickson, Robert Porter; Fiorenza, Maria Teresa
Decreased neural stem cell proliferation and olfaction in mouse models of Niemann–Pick C1 disease and the response to hydroxypropyl-β-cyclodextrin
2019 Dragotto, Jessica; Palladino, Giampiero; Canterini, Sonia; Caporali, Paola; Patil, Rutaraj; Fiorenza, Maria Teresa; Erickson, Robert P.
Neuronal dysfunction in Niemann Pick C1 disease: impact of early developmental defects and efficacy of hydroxypropyl-betacyclodextrin in correcting the phenotype.
2015 Canterini, Sonia; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Bruno, Francesco; Georgia, A; Loizzo, S; Erickson, Robert Porter; Fiorenza, Maria Teresa
Visual evoked potentials of Niemann-Pick type C1 mice reveal an impairment of the visual pathway that is rescued by 2-hydroxypropyl-ß-cyclodextrin
2015 Palladino, Giampiero; Loizzo, Stefano; Fortuna, Andrea; Canterini, Sonia; Palombi, Fioretta; Erickson, Robert Porter; Mangia, Franco; Fiorenza, Maria Teresa
| Titolo | Data di pubblicazione | Autore(i) | File |
|---|---|---|---|
| A novel approach to treat mitochondrial metabolism dysfunction in Niemann-Pick type C disease | 2024 | Tiberi, Jessica; Stefanelli, Roberta; Trenta, Francesco; LA ROSA, Piergiorgio; Siddlesh, Aras; Erickson, Robert; Grossmann, Lawrence I.; Fiorenza, Maria Teresa | |
| Altered Shh signaling at the primary cilium is responsible for abnormal cerebellum morphogenesis in Niemann-Pick C1 (NPC1) disease. | 2016 | Canterini, Sonia; Caporali, Paola; Bruno, Francesco; Dragotto, Jessica; Palladino, Giampiero; Dardis, A; Erickson, Robert Porter; Fiorenza, Maria Teresa | |
| Decreased neural stem cell proliferation and olfaction in mouse models of Niemann–Pick C1 disease and the response to hydroxypropyl-β-cyclodextrin | 2019 | Dragotto, Jessica; Palladino, Giampiero; Canterini, Sonia; Caporali, Paola; Patil, Rutaraj; Fiorenza, Maria Teresa; Erickson, Robert P. | |
| Neuronal dysfunction in Niemann Pick C1 disease: impact of early developmental defects and efficacy of hydroxypropyl-betacyclodextrin in correcting the phenotype. | 2015 | Canterini, Sonia; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Bruno, Francesco; Georgia, A; Loizzo, S; Erickson, Robert Porter; Fiorenza, Maria Teresa | |
| Visual evoked potentials of Niemann-Pick type C1 mice reveal an impairment of the visual pathway that is rescued by 2-hydroxypropyl-ß-cyclodextrin | 2015 | Palladino, Giampiero; Loizzo, Stefano; Fortuna, Andrea; Canterini, Sonia; Palombi, Fioretta; Erickson, Robert Porter; Mangia, Franco; Fiorenza, Maria Teresa |