CAPRINI, ELENA SOFIA
CAPRINI, ELENA SOFIA
DIPARTIMENTO DI BIOLOGIA E BIOTECNOLOGIE "CHARLES DARWIN"
Astrocytes differentiated from patient iPSCs model the rare leukodystrophy MLC and uncover disease-linked maturation defects and Kir4.1 channel dysfunction
2026 Lanciotti, Angela; Stefania Brignone, Maria; De Nuccio2, Chiara; Sposito, Sara; Caprini, Elena Sofia; Belfiore, Marcello; Nicita, Francesco; Veroni, Caterina; Meloni, Chiara; Carrozzo, Rosalba; Rizza, Teresa; Aiello, Chiara; Sartorelli, Jacopo; Bertini, Enrico; Visentin, Sergio; Elena Ambrosini, And
Development of 3D human cell culture models for studying MLC disease
2024 Caprini, E. S.; Lanciotti, A.; Brignone, M. S.; Serafini, B.; Rosicarelli, B.; Sposito, S.; Nicita, F.; Carrozzo, R.; Bertini, E.; Ambrosini, E.
Development of brain organoids from human induced pluripotent stem cells for studying the rare leukodystrophy megalencephalic leukoencephalopathy with subcortical cysts
2025 Caprini, E. S.; Lanciotti, A.; Brignone, M. S.; Rosicarelli, B.; Veroni, C.; Meloni, C.; Sposito, S.; Alfieri, L.; Scipioni, A.; Nicita, F.; Carrozzo, R.; Bertini, E.; Serafini, B.; Ambrosini, E.
Development of brain organoids from human induced pluripotent stem cells for studying the rare leukodystrophy megalencephalic leukoencephalopathy with subcortical cysts
2026 Caprini, Elena Sofia; Lanciotti, Angela; Brignone, Maria Stefania; Rosicarelli, Barbara; Veroni, Caterina; Meloni, Chiara; Sposito, Sara; Alfieri, Lavinia; Santia, Lorenzo; Scipioni, Angela; Nicita, Francesco; Bertini, Enrico; Serafini, Barbara; Ambrosini, Elena
Inducible pluripotent stem (iPS) cell-derived human astrocytes as a new disease model for the megalencephalic leukoencephalopathy with subcortical cysts (MLC): searching for shared pathological mechanisms of myelin degeneration in astrocytopathies
2025 Sposito, S.; Brignone, M. S.; Caprini, E. S.; Veroni, C.; Meloni, C.; De Nuccio, C.; Camerini, S.; Belfiore, M.; Nicita, F.; Bertini, E.; Ambrosini, E.; Lanciotti, A.
Megalencephalic leukoencephalopathy with subcortical cysts protein-1: A new calcium-sensitive protein functionally activated by endoplasmic reticulum calcium release and calmodulin binding in astrocytes
2024 Brignone, M. S.; Lanciotti, A.; Molinari, P.; Mallozzi, C.; De Nuccio, C.; Caprini, E. S.; Petrucci, T. C.; Visentin, S.; Ambrosini, E.
Role of Oxidative Stress in the Pathogenesis of Megalencephalic Leukoencephalopathy with Subcortical Cysts (MLC): exploring new molecular mechanisms using astrocytoma cell lines and iPSC-derived human astrocytes
2025 Sposito, S.; Brignone, M. S.; Caprini, E. S.; De Nuccio, C.; Greco, A.; Bernardo, A.; Molinari, P.; Nicita, F.; Camerini, S.; Carrozzo, R.; Bertini, E.; Lanciotti And E. Ambrosini., A.
| Titolo | Data di pubblicazione | Autore(i) | File |
|---|---|---|---|
| Astrocytes differentiated from patient iPSCs model the rare leukodystrophy MLC and uncover disease-linked maturation defects and Kir4.1 channel dysfunction | 2026 | Lanciotti, Angela; Stefania Brignone, Maria; De Nuccio2, Chiara; Sposito, Sara; Caprini, Elena Sofia; Belfiore, Marcello; Nicita, Francesco; Veroni, Caterina; Meloni, Chiara; Carrozzo, Rosalba; Rizza, Teresa; Aiello, Chiara; Sartorelli, Jacopo; Bertini, Enrico; Visentin, Sergio; Elena Ambrosini, And | |
| Development of 3D human cell culture models for studying MLC disease | 2024 | Caprini, E. S.; Lanciotti, A.; Brignone, M. S.; Serafini, B.; Rosicarelli, B.; Sposito, S.; Nicita, F.; Carrozzo, R.; Bertini, E.; Ambrosini, E. | |
| Development of brain organoids from human induced pluripotent stem cells for studying the rare leukodystrophy megalencephalic leukoencephalopathy with subcortical cysts | 2025 | Caprini, E. S.; Lanciotti, A.; Brignone, M. S.; Rosicarelli, B.; Veroni, C.; Meloni, C.; Sposito, S.; Alfieri, L.; Scipioni, A.; Nicita, F.; Carrozzo, R.; Bertini, E.; Serafini, B.; Ambrosini, E. | |
| Development of brain organoids from human induced pluripotent stem cells for studying the rare leukodystrophy megalencephalic leukoencephalopathy with subcortical cysts | 2026 | Caprini, Elena Sofia; Lanciotti, Angela; Brignone, Maria Stefania; Rosicarelli, Barbara; Veroni, Caterina; Meloni, Chiara; Sposito, Sara; Alfieri, Lavinia; Santia, Lorenzo; Scipioni, Angela; Nicita, Francesco; Bertini, Enrico; Serafini, Barbara; Ambrosini, Elena | |
| Inducible pluripotent stem (iPS) cell-derived human astrocytes as a new disease model for the megalencephalic leukoencephalopathy with subcortical cysts (MLC): searching for shared pathological mechanisms of myelin degeneration in astrocytopathies | 2025 | Sposito, S.; Brignone, M. S.; Caprini, E. S.; Veroni, C.; Meloni, C.; De Nuccio, C.; Camerini, S.; Belfiore, M.; Nicita, F.; Bertini, E.; Ambrosini, E.; Lanciotti, A. | |
| Megalencephalic leukoencephalopathy with subcortical cysts protein-1: A new calcium-sensitive protein functionally activated by endoplasmic reticulum calcium release and calmodulin binding in astrocytes | 2024 | Brignone, M. S.; Lanciotti, A.; Molinari, P.; Mallozzi, C.; De Nuccio, C.; Caprini, E. S.; Petrucci, T. C.; Visentin, S.; Ambrosini, E. | |
| Role of Oxidative Stress in the Pathogenesis of Megalencephalic Leukoencephalopathy with Subcortical Cysts (MLC): exploring new molecular mechanisms using astrocytoma cell lines and iPSC-derived human astrocytes | 2025 | Sposito, S.; Brignone, M. S.; Caprini, E. S.; De Nuccio, C.; Greco, A.; Bernardo, A.; Molinari, P.; Nicita, F.; Camerini, S.; Carrozzo, R.; Bertini, E.; Lanciotti And E. Ambrosini., A. |