BRUNO, FRANCESCO
BRUNO, FRANCESCO
A marked paucity of granule cells in the developing cerebellum of the Npc1(-/-) mouse is corrected by a single injection of hydroxypropyl-β-cyclodextrin.
2014 Nusca, Stefania; Canterini, Sonia; Palladino, Giampiero; Bruno, Francesco; Mangia, Franco; R. p., Erickson; Fiorenza, Maria Teresa
Abnormal BDNF signalling underscores defects of cerebellar development in a mouse model of Niemann-Pick type C1 disease
2016 Bruno, Francesco; Caporali, Paola; Palladino, Giampiero; Dragotto, Jessica; Canterini, Sonia; Fiorenza, Maria Teresa
Altered Shh signaling at the primary cilium is responsible for abnormal cerebellum morphogenesis in Niemann-Pick C1 (NPC1) disease.
2016 Canterini, Sonia; Caporali, Paola; Bruno, Francesco; Dragotto, Jessica; Palladino, Giampiero; Dardis, A; Erickson, Robert Porter; Fiorenza, Maria Teresa
Cerebellar Brain-Derived Neurotrophic Factor (BDNF) defects in a mouse model of a lysosomal lipid storage disease
2018 Lucarelli, Micaela; Bruno, Francesco; Fiorenza, Maria Teresa; Canterini, Sonia
Coronary CT angiography alone versus with CT perfusion: a systematic review and meta-analysis assessing approaches for chest pain
2025 D'Ascenzo, F.; Faletti, R.; Di Pietro, G.; Improta, R.; Bruno, F.; Schoepf, U. J.; Di Vita, U.; Giacobbe, F.; Nebiolo, M.; Siliano, S.; Solano, A.; Morena, A.; Pasinato, E.; Balducci, M.; Pagliassotto, I.; Cura, G. C.; Mohamed, M.; Sardella, G.; Galea, N.; Dewey, M.; Francone, M.; Mancone, M.; Fonio, P.; De Ferrari, G. M.; De Filippo, O.; Gatti, M.
Developmental delay in motor skill acquisition in Niemann-Pick C1 mice reveals abnormal cerebellar morphogenesis
2016 Caporali, Paola; Bruno, Francesco; Palladino, Giampiero; Dragotto, Jessica; Petrosini, Laura; Mangia, Franco; Erickson, Robert P; Canterini, Sonia; Fiorenza, Maria Teresa
ENLIGHTENING MOLECULAR MECHANISMS OF ABNORMAL CEREBELLUM DEVELOPMENT IN MOUSE MODELS OF HUMAN NIEMANN-PICK C 1 DISEASE: THE EFFICACY OF HYDROXYPROPYLBETACYCLODEXTRIN IN CORRECTING THE PHENOTYPE
2015 Canterini, Sonia; Nusca, Stefania; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Abate, Georgia; Bruno, Francesco; Robert, Erickson; Fiorenza, Maria Teresa
Impaired cerebellar granule neuron proliferation in Niemann-Pick C1 mice is corrected by a single hydroxyproplyl-betacyclodextrin injection
2013 Nusca, Stefania; Bruno, Francesco; Mangia, Franco; Robert P., Erickson2; Canterini, Sonia; Fiorenza, Maria Teresa
Morphofunctional impairment of neuronal and glial cells in the developing cerebellum of a mouse model of Niemann-Pick type C1 disease
2017 Bruno, Francesco
Neuronal dysfunction in Niemann Pick C1 disease: impact of early developmental defects and efficacy of hydroxypropyl-betacyclodextrin in correcting the phenotype.
2015 Canterini, Sonia; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Bruno, Francesco; Georgia, A; Loizzo, S; Erickson, Robert Porter; Fiorenza, Maria Teresa
| Titolo | Data di pubblicazione | Autore(i) | File |
|---|---|---|---|
| A marked paucity of granule cells in the developing cerebellum of the Npc1(-/-) mouse is corrected by a single injection of hydroxypropyl-β-cyclodextrin. | 2014 | Nusca, Stefania; Canterini, Sonia; Palladino, Giampiero; Bruno, Francesco; Mangia, Franco; R. p., Erickson; Fiorenza, Maria Teresa | |
| Abnormal BDNF signalling underscores defects of cerebellar development in a mouse model of Niemann-Pick type C1 disease | 2016 | Bruno, Francesco; Caporali, Paola; Palladino, Giampiero; Dragotto, Jessica; Canterini, Sonia; Fiorenza, Maria Teresa | |
| Altered Shh signaling at the primary cilium is responsible for abnormal cerebellum morphogenesis in Niemann-Pick C1 (NPC1) disease. | 2016 | Canterini, Sonia; Caporali, Paola; Bruno, Francesco; Dragotto, Jessica; Palladino, Giampiero; Dardis, A; Erickson, Robert Porter; Fiorenza, Maria Teresa | |
| Cerebellar Brain-Derived Neurotrophic Factor (BDNF) defects in a mouse model of a lysosomal lipid storage disease | 2018 | Lucarelli, Micaela; Bruno, Francesco; Fiorenza, Maria Teresa; Canterini, Sonia | |
| Coronary CT angiography alone versus with CT perfusion: a systematic review and meta-analysis assessing approaches for chest pain | 2025 | D'Ascenzo, F.; Faletti, R.; Di Pietro, G.; Improta, R.; Bruno, F.; Schoepf, U. J.; Di Vita, U.; Giacobbe, F.; Nebiolo, M.; Siliano, S.; Solano, A.; Morena, A.; Pasinato, E.; Balducci, M.; Pagliassotto, I.; Cura, G. C.; Mohamed, M.; Sardella, G.; Galea, N.; Dewey, M.; Francone, M.; Mancone, M.; Fonio, P.; De Ferrari, G. M.; De Filippo, O.; Gatti, M. | |
| Developmental delay in motor skill acquisition in Niemann-Pick C1 mice reveals abnormal cerebellar morphogenesis | 2016 | Caporali, Paola; Bruno, Francesco; Palladino, Giampiero; Dragotto, Jessica; Petrosini, Laura; Mangia, Franco; Erickson, Robert P; Canterini, Sonia; Fiorenza, Maria Teresa | |
| ENLIGHTENING MOLECULAR MECHANISMS OF ABNORMAL CEREBELLUM DEVELOPMENT IN MOUSE MODELS OF HUMAN NIEMANN-PICK C 1 DISEASE: THE EFFICACY OF HYDROXYPROPYLBETACYCLODEXTRIN IN CORRECTING THE PHENOTYPE | 2015 | Canterini, Sonia; Nusca, Stefania; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Abate, Georgia; Bruno, Francesco; Robert, Erickson; Fiorenza, Maria Teresa | |
| Impaired cerebellar granule neuron proliferation in Niemann-Pick C1 mice is corrected by a single hydroxyproplyl-betacyclodextrin injection | 2013 | Nusca, Stefania; Bruno, Francesco; Mangia, Franco; Robert P., Erickson2; Canterini, Sonia; Fiorenza, Maria Teresa | |
| Morphofunctional impairment of neuronal and glial cells in the developing cerebellum of a mouse model of Niemann-Pick type C1 disease | 2017 | Bruno, Francesco | |
| Neuronal dysfunction in Niemann Pick C1 disease: impact of early developmental defects and efficacy of hydroxypropyl-betacyclodextrin in correcting the phenotype. | 2015 | Canterini, Sonia; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Bruno, Francesco; Georgia, A; Loizzo, S; Erickson, Robert Porter; Fiorenza, Maria Teresa |