NUSCA, STEFANIA

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A marked paucity of granule cells in the developing cerebellum of the Npc1(-/-) mouse is corrected by a single injection of hydroxypropyl-β-cyclodextrin. 2014 Nusca, Stefania; Canterini, Sonia; Palladino, Giampiero; Bruno, Francesco; Mangia, Franco; R. p., Erickson; Fiorenza, Maria Teresa
ENLIGHTENING MOLECULAR MECHANISMS OF ABNORMAL CEREBELLUM DEVELOPMENT IN MOUSE MODELS OF HUMAN NIEMANN-PICK C 1 DISEASE: THE EFFICACY OF HYDROXYPROPYLBETACYCLODEXTRIN IN CORRECTING THE PHENOTYPE 2015 Canterini, Sonia; Nusca, Stefania; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Abate, Georgia; Bruno, Francesco; Robert, Erickson; Fiorenza, Maria Teresa
GRANULE NEURON PROLIFERATION IS REDUCED IN THE DEVELOPING CEREBELLUM OF THE NPC1-/- MOUSE, A MODEL OF HUMAN NIEMANN-PICK C1 DISEASE 2014 Canterini, Sonia; Palladino, Giampiero; Nusca, Stefania; Abate, Georgia; Mangia, Franco; R. P., Erickson; Fiorenza, Maria Teresa
Impact of the selenoprotein nGPx4 on male fertility and sperm epigenome. 2012 Pipolo, Simona; Puglisi, Rossella; Sodano, I; Nusca, Stefania; Mangia, Franco; Boitani, Carla
Impaired cerebellar granule neuron proliferation in Niemann-Pick C1 mice is corrected by a single hydroxyproplyl-betacyclodextrin injection 2013 Nusca, Stefania; Bruno, Francesco; Mangia, Franco; Robert P., Erickson2; Canterini, Sonia; Fiorenza, Maria Teresa
Male subfertility and sperm epigenome alterations in mice lacking the selenoprotein nGPx4 . 2012 Pipolo, Simona; Puglisi, Rossella; Sodano, I; Nusca, Stefania; Mangia, Franco; Boitani, Carla
Multiple TSC22D4 iso-/phospho-glycoforms display idiosyncratic subcellular localizations and interacting protein partners 2013 Canterini, Sonia; Carletti, Valentina; Nusca, Stefania; Mangia, Franco; Fiorenza, Maria Teresa
Niemann Pick C1 Gene Loss Of Function Impairs Cerebellar Foliation 2012 Nusca, Stefania; Canterini, Sonia; Mangia, Franco; Rp, Erickson; Fiorenza, Maria Teresa
Specific interaction of TSC22D4 forms with chromatin, mitochondrial apoptosis inducing factor and nuclear matrix in differentiated and apoptosis-committed cerebellar granule neurons. 2011 Canterini, Sonia; Nusca, Stefania; Carletti, Valentina; Mangia, F; Fiorenza, Maria Teresa
The tumor suppressor TSC22D4 and AIF associate in mitochondria and shift to different nuclear compartments at the onset of apoptosis 2012 Canterini, Sonia; Carletti, Valentina; Nusca, Stefania; Mangia, Franco; Fiorenza, Maria Teresa
TSC22D1 regulates cerebellum granule neurons differentiation by interacting with TSC22D4 and BKCa potassium channels. 2011 Carletti, Valentina; Canterini, Sonia; Nusca, Stefania; Mangia, F; Fiorenza, Maria Teresa