Background Ectodermal Dysplasias (EDs) are a large group of syndrome that are heterogeneous under clinical and genetic aspects, and are characterised by anomalies in the structures of ectodermal origin. In EDs dental anomalies in shape and number (oligo-hypodontia) occur frequently and severely and can affect both the primary and permanent dentition. Cas Report The oral habilitation of a child affected by X linked Hypohidrotic-Ectodermal Dyspasia with oligodontia over a period of ten years is described. This report includes discussion of the aetiology of EDs as well as discussion of the long term prognosis for the patient. Conclusion The success of treatment in the case reported is based on an early diagnosis and a correct timing of interventions addressing the preservation of the existing dental elements early functional rehabilitation and aesthetic correction.
X-linked Hypohidrotic Ectodermal Dysplasia: a ten-year case report and clinical considerations / S., Dall'Oca; E., Ceppi; Pompa, Giorgio; Polimeni, Antonella. - In: EUROPEAN JOURNAL OF PAEDIATRIC DENTISTRY. - ISSN 1591-996X. - STAMPA. - 9:4 Suppl(2008), pp. 14-18.
X-linked Hypohidrotic Ectodermal Dysplasia: a ten-year case report and clinical considerations
POMPA, Giorgio;POLIMENI, Antonella
2008
Abstract
Background Ectodermal Dysplasias (EDs) are a large group of syndrome that are heterogeneous under clinical and genetic aspects, and are characterised by anomalies in the structures of ectodermal origin. In EDs dental anomalies in shape and number (oligo-hypodontia) occur frequently and severely and can affect both the primary and permanent dentition. Cas Report The oral habilitation of a child affected by X linked Hypohidrotic-Ectodermal Dyspasia with oligodontia over a period of ten years is described. This report includes discussion of the aetiology of EDs as well as discussion of the long term prognosis for the patient. Conclusion The success of treatment in the case reported is based on an early diagnosis and a correct timing of interventions addressing the preservation of the existing dental elements early functional rehabilitation and aesthetic correction.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.