Hemangioendothelioma (HE) is the term used to name vascular neoplasms that show a borderline biological behaviour, intermediate between entirely benign hemangiomas and highly malignant angiosarcomas. The HE are classified in several types (papillary intralymphatic, kaposiform, epithelioid, retiform, pseudomyogenic and composite). Each of them have characteristic histo-pathological features and in the most of cases they present in childhood. The current scientific literature about HE is limited: infant and child case reports but lack of adult cases. In particularly no reported primary cardiac kaposiform HE has been described in the adult within nowadays. We analyzed all scientific literature and reported an outstanding and extremely rare case of primary cardiac kaposiform HE in the adult and make a comprehensive analysis of the scientific literature of this unusual interesting but not enough known issue.
Primary Cardiac Kaposiform Hemangioendothelioma: The Rare Adult-Onset. Review of the Literature / Lappa, Angela; Cottini, Marzia; Donfrancesco, Silvia; Feccia, Mariano; Pergolini, Amedeo; Polizzi, Vincenzo; Sbaraglia, Fabio; Distefano, Giada; Lilla Della Monica, Paola; Lucia Rosalba, Grillo; Musumeci, Francesco. - In: EC ANAESTHESIA. - ELETTRONICO. - 3:1(2017), pp. 4-17.
Primary Cardiac Kaposiform Hemangioendothelioma: The Rare Adult-Onset. Review of the Literature
Marzia Cottini;Silvia Donfrancesco;Amedeo Pergolini;
2017
Abstract
Hemangioendothelioma (HE) is the term used to name vascular neoplasms that show a borderline biological behaviour, intermediate between entirely benign hemangiomas and highly malignant angiosarcomas. The HE are classified in several types (papillary intralymphatic, kaposiform, epithelioid, retiform, pseudomyogenic and composite). Each of them have characteristic histo-pathological features and in the most of cases they present in childhood. The current scientific literature about HE is limited: infant and child case reports but lack of adult cases. In particularly no reported primary cardiac kaposiform HE has been described in the adult within nowadays. We analyzed all scientific literature and reported an outstanding and extremely rare case of primary cardiac kaposiform HE in the adult and make a comprehensive analysis of the scientific literature of this unusual interesting but not enough known issue.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.