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Mostrati risultati da 1 a 4 di 4
Neuronal dysfunction in Niemann Pick C1 disease: impact of early developmental defects and efficacy of hydroxypropyl-betacyclodextrin in correcting the phenotype.
2015 Canterini, Sonia; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Bruno, Francesco; Georgia, A; Loizzo, S; Erickson, Robert Porter; Fiorenza, Maria Teresa
Visual evoked potentials of Niemann-Pick type C1 mice reveal an impairment of the visual pathway that is rescued by 2-hydroxypropyl-ß-cyclodextrin
2015 Palladino, Giampiero; Loizzo, Stefano; Fortuna, Andrea; Canterini, Sonia; Palombi, Fioretta; Erickson, Robert Porter; Mangia, Franco; Fiorenza, Maria Teresa
Altered Shh signaling at the primary cilium is responsible for abnormal cerebellum morphogenesis in Niemann-Pick C1 (NPC1) disease.
2016 Canterini, Sonia; Caporali, Paola; Bruno, Francesco; Dragotto, Jessica; Palladino, Giampiero; Dardis, A; Erickson, Robert Porter; Fiorenza, Maria Teresa
Decreased neural stem cell proliferation and olfaction in mouse models of Niemann–Pick C1 disease and the response to hydroxypropyl-β-cyclodextrin
2019 Dragotto, Jessica; Palladino, Giampiero; Canterini, Sonia; Caporali, Paola; Patil, Rutaraj; Fiorenza, Maria Teresa; Erickson, Robert P.
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
Neuronal dysfunction in Niemann Pick C1 disease: impact of early developmental defects and efficacy of hydroxypropyl-betacyclodextrin in correcting the phenotype. | 2015 | Canterini, Sonia; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Bruno, Francesco; Georgia, A; Loizzo, S; Erickson, Robert Porter; Fiorenza, Maria Teresa | |
Visual evoked potentials of Niemann-Pick type C1 mice reveal an impairment of the visual pathway that is rescued by 2-hydroxypropyl-ß-cyclodextrin | 2015 | Palladino, Giampiero; Loizzo, Stefano; Fortuna, Andrea; Canterini, Sonia; Palombi, Fioretta; Erickson, Robert Porter; Mangia, Franco; Fiorenza, Maria Teresa | |
Altered Shh signaling at the primary cilium is responsible for abnormal cerebellum morphogenesis in Niemann-Pick C1 (NPC1) disease. | 2016 | Canterini, Sonia; Caporali, Paola; Bruno, Francesco; Dragotto, Jessica; Palladino, Giampiero; Dardis, A; Erickson, Robert Porter; Fiorenza, Maria Teresa | |
Decreased neural stem cell proliferation and olfaction in mouse models of Niemann–Pick C1 disease and the response to hydroxypropyl-β-cyclodextrin | 2019 | Dragotto, Jessica; Palladino, Giampiero; Canterini, Sonia; Caporali, Paola; Patil, Rutaraj; Fiorenza, Maria Teresa; Erickson, Robert P. |
Mostrati risultati da 1 a 4 di 4
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