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The neuroprotective effect of thiotaurine in potassium deprivation-induced apoptosis of cerebellar granule neurons 2014 Dragotto, Jessica; Capuozzo, Elisabetta; Fontana, Mario; Fiorenza, Maria Teresa; Canterini, Sonia
ANTAGONIST TSC22D VARIANTS CONTROL PROLIFERATION/DIFFERENTIATION SWITCH IN CEREBELLAR GRANULE NEURONS AND MEDULLOBLASTOMA CELLS 2014 Dragotto, Jessica; Canterini, Sonia; Palladino, Giampiero; Mangia, Franco; Fiorenza, Maria Teresa
Neuronal dysfunction in Niemann Pick C1 disease: impact of early developmental defects and efficacy of hydroxypropyl-betacyclodextrin in correcting the phenotype. 2015 Canterini, Sonia; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Bruno, Francesco; Georgia, A; Loizzo, S; Erickson, Robert Porter; Fiorenza, Maria Teresa
Thiotaurine protects mouse cerebellar granule neurons from potassium deprivation-induced apoptosis by inhibiting the activation of caspase-3 2015 Dragotto, Jessica; Capuozzo, Elisabetta; Fontana, Mario; Curci, Armando; Fiorenza, Maria Teresa; Canterini, Sonia
ENLIGHTENING MOLECULAR MECHANISMS OF ABNORMAL CEREBELLUM DEVELOPMENT IN MOUSE MODELS OF HUMAN NIEMANN-PICK C 1 DISEASE: THE EFFICACY OF HYDROXYPROPYLBETACYCLODEXTRIN IN CORRECTING THE PHENOTYPE 2015 Canterini, Sonia; Nusca, Stefania; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Abate, Georgia; Bruno, Francesco; Robert, Erickson; Fiorenza, Maria Teresa
Abnormal BDNF signalling underscores defects of cerebellar development in a mouse model of Niemann-Pick type C1 disease 2016 Bruno, Francesco; Caporali, Paola; Palladino, Giampiero; Dragotto, Jessica; Canterini, Sonia; Fiorenza, Maria Teresa
Shortened primary cilia length and altered Sonic hedgehog signaling in Niemann Pick C1 (NPC1) disease. 2016 Canterini, Sonia; Dragotto, Jessica; Zampieri, S; Dardis, A; Fiorenza, Maria Teresa
Developmental delay in motor skill acquisition in Niemann-Pick C1 mice reveals abnormal cerebellar morphogenesis 2016 Caporali, Paola; Bruno, Francesco; Palladino, Giampiero; Dragotto, Jessica; Petrosini, Laura; Mangia, Franco; Erickson, Robert P; Canterini, Sonia; Fiorenza, Maria Teresa
Altered Shh signaling at the primary cilium is responsible for abnormal cerebellum morphogenesis in Niemann-Pick C1 (NPC1) disease. 2016 Canterini, Sonia; Caporali, Paola; Bruno, Francesco; Dragotto, Jessica; Palladino, Giampiero; Dardis, A; Erickson, Robert Porter; Fiorenza, Maria Teresa
Role of TGF ß1 protein family members (TSC22D) in the control of cell proliferation/differentiation and apoptosis 2016 Dragotto, Jessica; Palladino, Giampiero; Mangia, F; Fiorenza, Maria Teresa; Canterini, Sonia
Shortened primary cilium length and dysregulated Sonic hedgehog signaling in Niemann-Pick C1 disease 2017 Canterini, Sonia; Dragotto, Jessica; Dardis, Andrea; Zampieri, Stefania; DE STEFANO, Maria Egle; Mangia, Franco; Erickson, Robert P.; Fiorenza, Maria Teresa
PATHOGENETIC MECHANISMS RESPONSIBLE FOR ALTERED DEVELOPMENTAL TRAJECTORIES IN NIEMANN PICK C DISEASE 2018 Canterini, Sonia; Dragotto, Jessica; Lucarelli, Micaela; Caporali, Paola; Rava, Alessandro; Fiorenza, Maria Teresa
Myo-inositol and D-chiro-inositol (40:1) reverse histological and functional features of polycystic ovary syndrome in a mouse model 2018 Bevilacqua, A.; Dragotto, J.; Giuliani, Alessandro; Bizzarri, M.
Linear cyclodextrin polymer prodrugs as novel yherapeutics for Niemann-Pick type C1 disorder 2018 Kulkarni, Aditya; Caporali, Paola; Dolas, Atul; Johny, Soniya; Goyal, Sandeep; Dragotto, Jessica; Macone, Alberto; Jayaraman, Ramesh; Fiorenza, Maria Teresa
The interplay between TGF-β-stimulated TSC22 domain family proteins regulates cell-cycle dynamics in medulloblastoma cells 2019 Dragotto, Jessica; Canterini, Sonia; Del Porto, Paola; Bevilacqua, Arturo; Fiorenza, Maria Teresa
Decreased neural stem cell proliferation and olfaction in mouse models of Niemann–Pick C1 disease and the response to hydroxypropyl-β-cyclodextrin 2019 Dragotto, Jessica; Palladino, Giampiero; Canterini, Sonia; Caporali, Paola; Patil, Rutaraj; Fiorenza, Maria Teresa; Erickson, Robert P.
The endocannabinoid system is affected by cholesterol dyshomeostasis: Insights from a murine model of Niemann Pick type C disease 2019 Oddi, S.; Caporali, P.; Dragotto, J.; Totaro, A.; Maiolati, M.; Scipioni, L.; Angelucci, C. B.; Orsini, C.; Canterini, S.; Rapino, C.; Maccarrone, M.; Fiorenza, M. T.
Decreased membrane cholesterol in liver mitochondria of the point mutation mouse model of juvenile Niemann–Pick C1, Npc1nmf164 2020 Erickson, Robert P; Aras, Siddhesh; Purandare, Neeraja; Hüttemann, Maik; Liu, Jenney; Dragotto, Jessica; Fiorenza, Maria Teresa; Grossman, Lawrence I.
High doses of d-chiro-inositol alone induce a pco-like syndrome and other alterations in mouse ovaries 2021 Bevilacqua, A.; Dragotto, J.; Lucarelli, M.; Di Emidio, G.; Monastra, G.; Tatone, C.
The appearance of phagocytic microglia in the postnatal brain of Niemann Pick type C mice is developmentally regulated and underscores shortfalls in fine odor discrimination 2022 Rava, Alessandro; La Rosa, Piergiorgio; Palladino, Giampiero; Dragotto, Jessica; Totaro, Antonio; Tiberi, Jessica; Canterini, Sonia; Oddi, Sergio; Fiorenza, Maria Teresa
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