Sfoglia per Autore
Impaired cerebellar granule neuron proliferation in Niemann-Pick C1 mice is corrected by a single hydroxyproplyl-betacyclodextrin injection
2013 Nusca, Stefania; Bruno, Francesco; Mangia, Franco; Robert P., Erickson2; Canterini, Sonia; Fiorenza, Maria Teresa
A marked paucity of granule cells in the developing cerebellum of the Npc1(-/-) mouse is corrected by a single injection of hydroxypropyl-β-cyclodextrin.
2014 Nusca, Stefania; Canterini, Sonia; Palladino, Giampiero; Bruno, Francesco; Mangia, Franco; R. p., Erickson; Fiorenza, Maria Teresa
Neuronal dysfunction in Niemann Pick C1 disease: impact of early developmental defects and efficacy of hydroxypropyl-betacyclodextrin in correcting the phenotype.
2015 Canterini, Sonia; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Bruno, Francesco; Georgia, A; Loizzo, S; Erickson, Robert Porter; Fiorenza, Maria Teresa
ENLIGHTENING MOLECULAR MECHANISMS OF ABNORMAL CEREBELLUM DEVELOPMENT IN MOUSE MODELS OF HUMAN NIEMANN-PICK C 1 DISEASE: THE EFFICACY OF HYDROXYPROPYLBETACYCLODEXTRIN IN CORRECTING THE PHENOTYPE
2015 Canterini, Sonia; Nusca, Stefania; Palladino, Giampiero; Dragotto, Jessica; Caporali, Paola; Abate, Georgia; Bruno, Francesco; Robert, Erickson; Fiorenza, Maria Teresa
Abnormal BDNF signalling underscores defects of cerebellar development in a mouse model of Niemann-Pick type C1 disease
2016 Bruno, Francesco; Caporali, Paola; Palladino, Giampiero; Dragotto, Jessica; Canterini, Sonia; Fiorenza, Maria Teresa
Developmental delay in motor skill acquisition in Niemann-Pick C1 mice reveals abnormal cerebellar morphogenesis
2016 Caporali, Paola; Bruno, Francesco; Palladino, Giampiero; Dragotto, Jessica; Petrosini, Laura; Mangia, Franco; Erickson, Robert P; Canterini, Sonia; Fiorenza, Maria Teresa
Altered Shh signaling at the primary cilium is responsible for abnormal cerebellum morphogenesis in Niemann-Pick C1 (NPC1) disease.
2016 Canterini, Sonia; Caporali, Paola; Bruno, Francesco; Dragotto, Jessica; Palladino, Giampiero; Dardis, A; Erickson, Robert Porter; Fiorenza, Maria Teresa
Morphofunctional impairment of neuronal and glial cells in the developing cerebellum of a mouse model of Niemann-Pick type C1 disease
2017 Bruno, Francesco
Cerebellar Brain-Derived Neurotrophic Factor (BDNF) defects in a mouse model of a lysosomal lipid storage disease
2018 Lucarelli, Micaela; Bruno, Francesco; Fiorenza, Maria Teresa; Canterini, Sonia
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