Sfoglia per Rivista HAEMOPHILIA
acokinetics of reformulated B-domain deleted recombinant factor VIII (BDD-rFVIII) concentrate using chromogenic and one-stage assays with pooled normal plasma (PNP) and refacto laboratory standard (RLS)
2008 Santoro, Cristina; Ferrante, F.; Iorio, A.; Biondo, F.; Pignoloni, P.; Mazzucconi, Maria Gabriella
Acquired haemophilia in severe pelvic endometriosis: a new association?
2012 A., Ferrari; Esmeralda, Conte; M. l., Troccoli; Nobili, Flavia; Marziani, Rosalia; Roberti, Claudia; Mossa, Bruno; Mazzucconi, Maria Gabriella; Lukic, Ankica; Moscarini, Massimo
ACQUIRED INHIBITOR AGAINST FACTOR IX IN A CHILD: SUCCESSFUL TREATMENT WITH HIGH-DOSE IMMUNOGLOBULINE AND DEXAMETHASONE
1999 Mazzucconi, Maria Gabriella; Peraino, M; Bizzoni, L; Bernasconi, S; Luciani, M; DE ROSSI, G.
Addressing current challenges in haemophilia care. consensus recommendations of a european interdisciplinary working group
2005 Ludlam, C. A.; Mannucci, P. M.; Powderly, W. G.; Roca, C. A.; Astermark, J.; Auerswald, G.; Garcia Barrios, M.; Chistolini, A.; Dolan, G.; Gringeri, A.; Hermans, C.; Laurian, Y.; Lopez, R. P.; Peerlinck, K.; Pollmann, H.; Ritchie, B.; Rocino, A.; Schramm, W.; Tagliaferri, A.; Thomas, A. E.; Villar, A.; von Depka, M.; Heinz, F. X.; Kreil, T.; Kretzschmar, H. A.; Simmonds, P.; Soriano, V.; Lambden, P.; Mantovani, L. A.; Schmid, G.
Application of Global Coagulation Assays in Hemophilia B Patients to Evaluate the Hemostatic Potential in Baseline Conditions
2017 Ferrara, G; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; Baldacci, Erminia; Abbruzzese, R; Ferretti, Antonietta; Porrazzo, Marika; Mazzucconi, Maria Gabriella; Santoro, Cristina
Application of global coagulation assays in Hemophilia B patients to evaluate the hemostatic potential in baseline conditions and after FIX concentrate administration
2016 Santoro, Cristina; Ferrara, G; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; Baldacci, Erminia; Abbruzzese, R; Chisini, Marta; Basso, M; Mattone, Pf; Mazzucconi, Maria Gabriella
Bioequivalence of B-domain deleted and plasma derived FVIII concentrates
2010 M., Morfini; A., Iorio; Mazzucconi, Maria Gabriella; S., Cinotti; E., Zanon; E., Paladino
Bleeding phenotype and correlation with factor XI (FXI) activity in congenital FXI deficiency: Results of a retrospective study from a single centre
2015 Santoro, Cristina; DI MAURO, Roberta; Baldacci, E.; DE ANGELIS, Federico; Abbruzzese, R.; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; Ferrara, G.; Guarini, Anna; Foa, Roberto; Mazzucconi, Maria Gabriella
A Case Of Thrombosis In Congenital Afibrinogenemia: A Physiopathologic And Management Dilemma
2015 Santoro, Cristina; Massaro, Fulvio; Capria, S; Venosi, Salvatore; Baldacci, Erminia; Abbruzzese, R; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; De Angelis, F; Volpicelli, P; Mazzucconi, Maria Gabriella
Clinical efficacy of highly purified, doubly virus-inactivated factor VIII/von Willebrand factor concentrate (Fanhdi) in the treatment of von Willebrand disease: a retrospective clinical study
2002 Federici, Ab; Baudo, F; Caracciolo, C; Mancuso, G; Mazzucconi, Mg; Musso, R; Schinco, Pc; Targhetta, R; Marcucci, Pm
Congenital FXI Deficiency: Preliminary Results Of Phenotypic (Clinical And Laboratory) And Genotypic Characterization Of A Case Series From A Single Center
2015 Santoro, Cristina; Di Mauro, R; Bicocchi, P; Acquila, M; Baldacci, Erminia; Basso, M; Abbruzzese, R; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; Ferrara, G; Volpicelli, P; Mazzucconi, Maria Gabriella
Correlation of bleeding phenotype/FXI activity (FXI:Act) in congenital FXI deficiency.
2014 Santoro, Cristina; DI MAURO, Roberta; E., Baldacci; F., De Angelis; R., Abbruzzese; Barone, Francesco; R. A., Bochicchio; L., Parlanti; Foa, Roberto; Mazzucconi, Maria Gabriella
Cost-effectiveness analysis of late prophylaxis vs. on-demand treatment for severe haemophilia A in Italy
2017 Coppola, A.; D'Ausilio, Alessandro; Aiello, A.; Amoresano, S.; Toumi, M.; Mathew, P.; Tagliaferri, A; Feola, G.; Molinari, A. C.; Santoro, Cristina; Rivolta, G. F.; Cultrera, D. B.; Gagliano, F.; Zanon, E.; Mancuso, M. E.; Valdrè, L.; Mameli, L.; Banov, L.; Di Minno, G.; Quintavalle, G.; Mazzucconi, Maria Gabriella; Negri, N.; Santagostino, E.
Dental invasive procedures in hemophilia A/B (HA/HB) and von Willebrand disease (VWD) patients: Experience of a single centre
2012 D., Gaglioti; V., De Padua; R., Bosco; F., Riva; Santoro, Cristina; F., Biondo; E., Baldacci; Mazzucconi, Maria Gabriella
Different prophylaxis regimens in young severe hemophilia A patients: efficacy, FVIII consumption, and therapy compliance
2012 F., Biondo; Santoro, Cristina; E., Baldacci; A., Leporace; R., Foa; Mazzucconi, Maria Gabriella
Different regimens of prophylaxis treatment in young severe hemophilia A patients: comparisons on efficacy, FVIII consumption, and therapy compliance
2010 Biondo, F; Santoro, Cristina; Baldacci, Erminia; Torelli, F; Leporace, Annapaola; Mazzucconi, Maria Gabriella
Effects of secondary prophylaxis started in adolescent and adult haemophiliacs
2008 Tagliaferri, Annarita; Franchini, M.; Coppola, A.; Rivolta, G. F.; Santoro, Cristina; Rossetti, G.; Feola, G.; Zanon, E.; Dragani, A.; Iannaccaro, P.; Radossi, P.; Mannucci, P. M.
Efficacy and safety during formulation switch of a pasteurized VWF/FVIII concentrate: results from an Italian prospective observational study in patients with von Willebrand disease.
2013 Castaman, G; Coppola, A; Zanon, E; Boeri, E; Musso, M; Siragusa, S; Federici, Ab; Mancuso, G; Barillari, G; Biasoli, C; Feola, G; Franchini, M; Moratelli, S; Gamba, G; Schinco, P; Valdrè, L; Dragani, A; Mazzucconi, Maria Gabriella; Tagliaferri, A; Morfini, M.
Efficacy and safety of antithrombotic prophylactic therapy with low-molecular weight heparin (LMWH) after orthopedic surgery in hemophilia patients
2012 F., Biondo; E., Baldacci; F., Lacava; Santoro, Cristina; A., Leporace; L., Poggini; F., Falez; A., Antonaci; R., Foa; Mazzucconi, Maria Gabriella
Efficacy and safety of highly purified VWF/FVIII concentrates in the treatment of inherited von Willebrand disease: results from the retrospective Italian study on 120 cases
2008 A., Federici; G., Barillari; E., Zanon; Mazzucconi, Maria Gabriella; R., Musso; G., Castaman; P., Mannucci
Titolo | Data di pubblicazione | Autore(i) | File |
---|---|---|---|
acokinetics of reformulated B-domain deleted recombinant factor VIII (BDD-rFVIII) concentrate using chromogenic and one-stage assays with pooled normal plasma (PNP) and refacto laboratory standard (RLS) | 2008 | Santoro, Cristina; Ferrante, F.; Iorio, A.; Biondo, F.; Pignoloni, P.; Mazzucconi, Maria Gabriella | |
Acquired haemophilia in severe pelvic endometriosis: a new association? | 2012 | A., Ferrari; Esmeralda, Conte; M. l., Troccoli; Nobili, Flavia; Marziani, Rosalia; Roberti, Claudia; Mossa, Bruno; Mazzucconi, Maria Gabriella; Lukic, Ankica; Moscarini, Massimo | |
ACQUIRED INHIBITOR AGAINST FACTOR IX IN A CHILD: SUCCESSFUL TREATMENT WITH HIGH-DOSE IMMUNOGLOBULINE AND DEXAMETHASONE | 1999 | Mazzucconi, Maria Gabriella; Peraino, M; Bizzoni, L; Bernasconi, S; Luciani, M; DE ROSSI, G. | |
Addressing current challenges in haemophilia care. consensus recommendations of a european interdisciplinary working group | 2005 | Ludlam, C. A.; Mannucci, P. M.; Powderly, W. G.; Roca, C. A.; Astermark, J.; Auerswald, G.; Garcia Barrios, M.; Chistolini, A.; Dolan, G.; Gringeri, A.; Hermans, C.; Laurian, Y.; Lopez, R. P.; Peerlinck, K.; Pollmann, H.; Ritchie, B.; Rocino, A.; Schramm, W.; Tagliaferri, A.; Thomas, A. E.; Villar, A.; von Depka, M.; Heinz, F. X.; Kreil, T.; Kretzschmar, H. A.; Simmonds, P.; Soriano, V.; Lambden, P.; Mantovani, L. A.; Schmid, G. | |
Application of Global Coagulation Assays in Hemophilia B Patients to Evaluate the Hemostatic Potential in Baseline Conditions | 2017 | Ferrara, G; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; Baldacci, Erminia; Abbruzzese, R; Ferretti, Antonietta; Porrazzo, Marika; Mazzucconi, Maria Gabriella; Santoro, Cristina | |
Application of global coagulation assays in Hemophilia B patients to evaluate the hemostatic potential in baseline conditions and after FIX concentrate administration | 2016 | Santoro, Cristina; Ferrara, G; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; Baldacci, Erminia; Abbruzzese, R; Chisini, Marta; Basso, M; Mattone, Pf; Mazzucconi, Maria Gabriella | |
Bioequivalence of B-domain deleted and plasma derived FVIII concentrates | 2010 | M., Morfini; A., Iorio; Mazzucconi, Maria Gabriella; S., Cinotti; E., Zanon; E., Paladino | |
Bleeding phenotype and correlation with factor XI (FXI) activity in congenital FXI deficiency: Results of a retrospective study from a single centre | 2015 | Santoro, Cristina; DI MAURO, Roberta; Baldacci, E.; DE ANGELIS, Federico; Abbruzzese, R.; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; Ferrara, G.; Guarini, Anna; Foa, Roberto; Mazzucconi, Maria Gabriella | |
A Case Of Thrombosis In Congenital Afibrinogenemia: A Physiopathologic And Management Dilemma | 2015 | Santoro, Cristina; Massaro, Fulvio; Capria, S; Venosi, Salvatore; Baldacci, Erminia; Abbruzzese, R; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; De Angelis, F; Volpicelli, P; Mazzucconi, Maria Gabriella | |
Clinical efficacy of highly purified, doubly virus-inactivated factor VIII/von Willebrand factor concentrate (Fanhdi) in the treatment of von Willebrand disease: a retrospective clinical study | 2002 | Federici, Ab; Baudo, F; Caracciolo, C; Mancuso, G; Mazzucconi, Mg; Musso, R; Schinco, Pc; Targhetta, R; Marcucci, Pm | |
Congenital FXI Deficiency: Preliminary Results Of Phenotypic (Clinical And Laboratory) And Genotypic Characterization Of A Case Series From A Single Center | 2015 | Santoro, Cristina; Di Mauro, R; Bicocchi, P; Acquila, M; Baldacci, Erminia; Basso, M; Abbruzzese, R; Barone, Francesco; Bochicchio, RAFFAELE ANGELO; Ferrara, G; Volpicelli, P; Mazzucconi, Maria Gabriella | |
Correlation of bleeding phenotype/FXI activity (FXI:Act) in congenital FXI deficiency. | 2014 | Santoro, Cristina; DI MAURO, Roberta; E., Baldacci; F., De Angelis; R., Abbruzzese; Barone, Francesco; R. A., Bochicchio; L., Parlanti; Foa, Roberto; Mazzucconi, Maria Gabriella | |
Cost-effectiveness analysis of late prophylaxis vs. on-demand treatment for severe haemophilia A in Italy | 2017 | Coppola, A.; D'Ausilio, Alessandro; Aiello, A.; Amoresano, S.; Toumi, M.; Mathew, P.; Tagliaferri, A; Feola, G.; Molinari, A. C.; Santoro, Cristina; Rivolta, G. F.; Cultrera, D. B.; Gagliano, F.; Zanon, E.; Mancuso, M. E.; Valdrè, L.; Mameli, L.; Banov, L.; Di Minno, G.; Quintavalle, G.; Mazzucconi, Maria Gabriella; Negri, N.; Santagostino, E. | |
Dental invasive procedures in hemophilia A/B (HA/HB) and von Willebrand disease (VWD) patients: Experience of a single centre | 2012 | D., Gaglioti; V., De Padua; R., Bosco; F., Riva; Santoro, Cristina; F., Biondo; E., Baldacci; Mazzucconi, Maria Gabriella | |
Different prophylaxis regimens in young severe hemophilia A patients: efficacy, FVIII consumption, and therapy compliance | 2012 | F., Biondo; Santoro, Cristina; E., Baldacci; A., Leporace; R., Foa; Mazzucconi, Maria Gabriella | |
Different regimens of prophylaxis treatment in young severe hemophilia A patients: comparisons on efficacy, FVIII consumption, and therapy compliance | 2010 | Biondo, F; Santoro, Cristina; Baldacci, Erminia; Torelli, F; Leporace, Annapaola; Mazzucconi, Maria Gabriella | |
Effects of secondary prophylaxis started in adolescent and adult haemophiliacs | 2008 | Tagliaferri, Annarita; Franchini, M.; Coppola, A.; Rivolta, G. F.; Santoro, Cristina; Rossetti, G.; Feola, G.; Zanon, E.; Dragani, A.; Iannaccaro, P.; Radossi, P.; Mannucci, P. M. | |
Efficacy and safety during formulation switch of a pasteurized VWF/FVIII concentrate: results from an Italian prospective observational study in patients with von Willebrand disease. | 2013 | Castaman, G; Coppola, A; Zanon, E; Boeri, E; Musso, M; Siragusa, S; Federici, Ab; Mancuso, G; Barillari, G; Biasoli, C; Feola, G; Franchini, M; Moratelli, S; Gamba, G; Schinco, P; Valdrè, L; Dragani, A; Mazzucconi, Maria Gabriella; Tagliaferri, A; Morfini, M. | |
Efficacy and safety of antithrombotic prophylactic therapy with low-molecular weight heparin (LMWH) after orthopedic surgery in hemophilia patients | 2012 | F., Biondo; E., Baldacci; F., Lacava; Santoro, Cristina; A., Leporace; L., Poggini; F., Falez; A., Antonaci; R., Foa; Mazzucconi, Maria Gabriella | |
Efficacy and safety of highly purified VWF/FVIII concentrates in the treatment of inherited von Willebrand disease: results from the retrospective Italian study on 120 cases | 2008 | A., Federici; G., Barillari; E., Zanon; Mazzucconi, Maria Gabriella; R., Musso; G., Castaman; P., Mannucci |
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